Iridocorneal endothelial syndrome – A case of contradictions

Abstract

Iridocorneal endothelial syndrome comprises a spectrum of disorders, which present with features of corneal edema, iris atrophy, peripheral anterior synechiae, and secondary glaucoma, in varying combinations. Clinical variants include Chandler's syndrome, progressive iris atrophy, and Cogan-Reese/iris nevus syndrome. Although classically described as a unilateral condition in young women, bilaterality, varied age of presentation, and male gender are also possibilities. Here, we report a case of bilateral progressive iris atrophy in an elderly male.