Intracranial Dural Arteriovenous Shunts in Children

Abstract

Intracranial dural arteriovenous shunts (DAVS) are a group of different nosologic entities sharing a similar angioarchitecture1. In the pediatric recognized (table ​(table11)2. The neonatal-type (NDAVS) is characterized by a malformation of the dural sinuses (figures ​(figures1A1A,​,B).B). The most common symptoms are related to increased intracranial pressure (ICP), mild cardiac failure and coagulation disorders. The reduction of venous outlets of the brain and additional overload into the sinuses lead to spontaneous thrombosis and consequent occlusion of all venous outlets as well as coagulation consumption syndromes. Table 1 Classification of DAVS in the pediatric population2 * Figure 1 Neonatal-type DAVS (Case 5) A) Right occipital arteriogram (AP view) shows fistula from the occipital artery into a large, malformed dural sinus. B) Venous phase of right occipital arteriogram (lateral view) shows an occluded right transverse sinus (arrowhead) and a stenotic left jugular bulb (arrowhead).