INTRA-ABDOMINAL DESMOID TUMOUR- A RARE CASE REPORT WITH REVIEW OF LITERATURE.

Abstract

Introduction: Desmoid tumours (DTs) are benign, slowly growing deep seated monoclonal myo-fibroblastic neoplasms. It arises from musculoaponeurotic stromal elements. The incidence in the general population is 2-4 cases per million people per year. DTs are typically sporadic; and can occur anywhere in the body. A 30 year male patient presented with a giant intraabdominal DT is discussed here with review of available literature. DTs areDiscussion: benign, deep-seated slowly growing monoclonal myo-fibroblastic neoplasms arise from musculoaponeurotic stromal elements. Diagnosis may be confirmed with biopsy and immunohistochemistry. Preoperative assessment with MRI, CT with angiogram are imperative for definitive surgical resection. There are roles of chemotherapy and radiation therapy in management of primary and recurrent lesions. The surgical resection remains the mainstay of its management. Conclusions: The management of DT is challenging. Surgical resection is the cornerstone of its management. Chemotherapy and radiation therapy in management of primary and recurrent lesions may be considered.