Interrupted aortic arch with bicuspid aortic valve stenosis in an adult: A case report.

Abstract

The case report describes a rare instance of an interrupted aortic arch (IAA) with bicuspid aortic valve stenosis in a 48-year-old male patient with a one-year history of refractory hypertension, chest pain, and numbness in the upper and lower extremities. A single-stage operation was performed through a midline sternotomy, involving aortic valve replacement and posterior pericardial ascending-to-descending aortic bypass. Managing such rare conditions can be challenging due to limited guidelines, no meaningful conclusion may be made as to whether single-stage or two-stage repair is superior. Final management decision in adult patients with IAA must be individualized and depend on the associated malformations, patient preference, and precise anatomy imaging. The single-stage posterior pericardial ascending-to-descending aortic bypass appears as a safe surgical method in such cases when concomitant cardiac procedures are indicated.