Abstract

Ganglioneuroma is a rare benign tumor originates from neurol crest and may develop anywhere along the sympathetic nervous system is present. Nearly all patients with ganglioneuroma are older than 10 years old. In most cases ganlioneuromas are detected incidentally during work-up for unrelated conditions. Nevertheless, radiological and differential diagnosis of retroperitoneal masses may be challenging. We present management of a 6-year-old boy with ganglioneuroma that located in left retroperitoneum.

Highlights

  • Ganglineuroma (GN) is a rare benign tumor originates from neural crest cells that forms the sympathetic-adrenal system [1]

  • GNs may develop anywhere along the sympathetic nervous system is present, including cervical spine, mediastinum, retroperitoneum, or pelvis. 52% of GNs are detected in the abdomen (49% arise in the adrenal gland and %51 extra-adrenal), 39% in the mediastinum, and the remaining 9% are detected in the pelvis or neck [5]

  • We present a case of a large incidental tumor that located in retroperitoneum at the neighborhood of the upper pole of left kidney, in a 6-year-old boy

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Summary

Introduction

Ganglineuroma (GN) is a rare benign tumor originates from neural crest cells that forms the sympathetic-adrenal system [1]. In most cases GNs are detected incidentally during work-up for unrelated. We present a case of a large incidental tumor that located in retroperitoneum at the neighborhood of the upper pole of left kidney, in a 6-year-old boy. Case report In March 2015, a 7 cm-diameter mass adjacent to the upper pole of the left kidney was incidentally detected in a 6-year-old boy during examination in the emergency room for a non-vehicle traffic accident. On admission a retroperitoneal mass on the left side adjacent to upper pole of the kidney was recognized on computed tomography (CT), due to insufficient image quality of CT, a contrast magnetic resonance imaging (MRI) of the abdomen was performed and a serum panel was ordered to determine whether the mass was endocrinologically active. The patient died on January 2016, due to fall from a height

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