Imaging of Fibrous Dysplasia Protuberans, an Extremely Rare Exophytic Variant of Fibrous Dysplasia.

Amin Haghighat Jahromi,Michael D Starsiak,William F James,Eugene D Silverman

doi:10.3390/diagnostics11061006

Amin Haghighat Jahromi, Michael D Starsiak + Show 2 more

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https://doi.org/10.3390/diagnostics11061006

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Abstract

This paper details the case report of a 26-year-old man who presented with a growing right-sided skull mass evaluated with ultrasound, non-contrast CT, contrast-enhanced MRI and 99mTc-MDP whole body bone scan with SPECT/CT. These studies suggested a broad differential diagnosis favoring benign osseous lesions. Given a more recent increase in the rate of growth, headache and large size, the lesion was excised via craniotomy followed by cranioplasty. Pathology confirmed fibrous dysplasia (FD) as the diagnosis. Interestingly, this report is the imaging evaluation of the exophytic subtype of FD, the so-called FD protuberance, an extremely rare variant of FD, of which only two case reports are found in the literature.

Highlights

This paper details the case report of a 26-year-old man who presented with a growing right-sided skull mass evaluated with ultrasound, non-contrast CT, contrast-enhanced MRI and
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Given theosseous recent benign osseous lesions as osteochondroma, enchondroma protuberans, and surface osteoma, over less likely malignant such as parostealwas osteosarcoma increase in the of growth, headache and large size, the lesion was excised via craniotomy followed by cranioplasty