Abstract
Immunoglobulin G4 (IgG4)-related systematic disease (IgG4-RSD) is a systemic fibroinflammatory condition characterized by extensive IgG4-positive plasma cells and T-lymphocyte infiltration of various organs including pancreas, bile duct, gallbladder, salivary glands, kidney, lung, prostate, retroperitoneum and even the thyroid gland. It may affect one or two and sometimes more than three organs. Early diagnosis and treatment could not prevent sclerosis and permanent damage of the affected organ but also avoid other organ involvement. Here we present a rare case of IgG4-RSD affecting pancreas, biliary duct system and abdominal aorta. A review of the literature was also made mainly concerning IgG4-related sclerosing cholangitis (IgG4-SC) and periaortitis.
Sign-in/Register to access full text options 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
