Abstract
Gas chromatography was used for the determination of monosaccharides obtained by depolymerization of acid mucopolysaccharides (AMPS). Purified AMPS and AMPS precipitated from the urine of patients with mucopolysaccharidoses can be identified in this manner. The utility of the technique was illustrated by demonstrating the difference in the hexose-hexosamine pattern obtained by depolymerization of urinary AMPS from patients with Hurler's and Sanfilippo's disease. The diagnostic value of the technique in delineating more subtle differences in relative amounts of AMPS awaits further experimentation.
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