Hypoxemia and Right-to-Left-Shunt in Patient with Antiphospholipid Syndrome: A Case Report with Multimodality Imaging Findings and Literature Review.

Mnahi Bin Saeedan,Mashael Alrujaib,Ahmed L Fathala

doi:10.1155/2016/2092084

Mnahi Bin Saeedan, Mashael Alrujaib + Show 1 more

Open Access

https://doi.org/10.1155/2016/2092084

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Abstract

This is a case report of an extremely rare cause of superior vena cava syndrome with systemic-to-pulmonary venous shunts, illustrated using different imaging modalities with successful SVC and IVC dilatation and stenting.

Highlights

Superior vena cava (SVC) obstruction might be caused by different etiologies
We present a rare cause of Systemic-topulmonary venous shunts (SPVS) in patient with antiphospholipid syndrome, Budd-Chiari Syndrome, and SVC obstruction which was successfully treated with SVC and IVC dilatation and stenting
We present a case of antiphospholipid syndrome causing BCS with IVC and SVC thrombosis with progressive shortness of breath and hypoxemia due to SVC syndrome and SPVS

Summary

Introduction

Superior vena cava (SVC) obstruction might be caused by different etiologies. Lung cancer and lymphoma are the most frequent causes. Other benign processes such as central venous catheter and fibrosing mediastinitis can cause SVC obstruction. Collateral venous channels are usually formed to restore venous return [1,2,3,4]. Systemic-topulmonary venous shunts (SPVS) might be developed in case of severe and long-standing SVC obstruction [5–9]. We present a rare cause of SPVS in patient with antiphospholipid syndrome, Budd-Chiari Syndrome, and SVC obstruction which was successfully treated with SVC and IVC dilatation and stenting. We illustrated the SVC obstruction and SPVS using different imaging modalities

Case Report

Discussion

Conclusion