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Abstract
Amelogenesis imperfecta is an unusual hereditory disorder affecting both primary and permanent dentition. We present a rare case of hypocalcified auto-somal recessive amelogenesis imperfecta occuring in primary dentition in a 7-year-old girl with a family history of consanguineous marriage. Clinical and radiological examination revealed discoloration and hypoplasia of enamel with easy chipping affecting both maxillary and mandibular dentition.
Highlights
Amelogenesis imperfect (AI) encompasses a heterogeneous group of developmental disorders that demonstrate alterations in the enamel
We present a rare case of hypocalcified autosomal recessive amelogenesis imperfecta occuring in primary dentition in a 7-year-old girl with a family history of consanguineous marriage
Witkop and Sauk listed the varieties of AI, divided according to whether the abnormality lay in a reduced amount of enamel, deficient calcification, or imperfecta maturation of the enamel, and recognized the combined defects [3]
Summary
Amelogenesis imperfect (AI) encompasses a heterogeneous group of developmental disorders that demonstrate alterations in the enamel. Amelogenesis imperfecta (AI) is a group of conditions, genetic in origin, which affect the structure and clinical appearance of the enamel of all or most the teeth [3]. AI encompasses a complicated group of conditions that demonstrate developmental alterations in the structure of the enamel in the absence of a systemic disorder [4]. This enamel anomaly affects both primary and permanent dentition. Dental problems, which depend on the severity of the condition, include sensitive teeth and poor appearance due to tooth loss and staining. Attention must be paid to the psychological health of the patient [8]
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