Abstract
Situs inversus totalis is a very rare anomaly. Even more, cases of situs inversus totalis plus hypertrophic osteoarthropathy. A woman presented with cyanosis, clubbing of fingers and distal edema. Chest examination revealed heart sounds at the right side and a heart murmur. Abdominal examination showed liver dullness in the left side. The X-rays showed dextrocardia and liver in the left side. The Upper digestive barium test showed the stomach in the right side, the barium enema showed caecum on the left. Treatment for heart failure improved the patient’s condition and she remained well. When she became pregnant, developed heart failure again and required admission. She was compensated and continued her pregnancy. 3 years later she developed heart and respiratory refractory failure, was admitted again and after few days she died. We report this case of situs inversus totalis in association with hypertrophic osteoarthropathy because of the rarity of this anomaly.
Highlights
INTRODUCTIONSitus inversus totalis is a congenital anomaly occurring in 1 in 10,000 - 50,000 live births [1]; the condition is defined by a complete mirror image of the thoracic and abdominal viscera
A woman presented with cyanosis, clubbing of fingers and distal edema
When she became pregnant, developed heart failure again and required admission. She was compensated and continued her pregnancy. 3 years later she developed heart and respiratory refractory failure, was admitted again and after few days she died. We report this case of situs inversus totalis in association with hypertrophic osteoarthropathy because of the rarity of this anomaly
Summary
Situs inversus totalis is a congenital anomaly occurring in 1 in 10,000 - 50,000 live births [1]; the condition is defined by a complete mirror image of the thoracic and abdominal viscera. Affected patients may appear healthy, with no differences in their life expectancy. In some cases patients present additional hearth anomalies, such as interatrial communication. The systematic search of the literature did not disclose cases of situs inversus totalis plus hypertrophic osteoarthropathy. This case probably is the first report.
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