Abstract
BackgroundAngiomatoid fibrous histiocytoma (AFH) is a soft-tissue tumor that generally affects the extremities of children and young adults. AFH overlaps with primary pulmonary myxoid sarcoma (PPMS) and can occur in unusual locations.Case presentationWe present a case of a 22-year-old female with AFH in the distal trachea. In addition to describing the challenge in making a correct diagnosis of AFH, we describe the first case of successful hybrid bronchoscopic and surgical resection of endotracheal AFH. A staged removal procedure was required to quickly secure the airway, allowing a lower-risk elective distal tracheal resection through a cervical approach for complete resection. A more conventional, but more invasive, more painful and cosmetically less satisfying thoracotomy was avoided.ConclusionsA distal tracheal resection for AFH can be safely performed in young adults through a cervical approach with excellent follow-up results.
Highlights
Angiomatoid fibrous histiocytoma (AFH) is a soft-tissue tumor that generally affects the extremities of children and young adults, but occasionally occurs at unusual locations such as the trachea [1,2,3]
This case-report demonstrates the challenge in making a correct diagnosis of endotracheal AFH and presents the first case of successful hybrid bronchoscopic and surgical resection of endotracheal AFH
The remaining tumor was removed through a cervical approach with a partial distal tracheal resection and end-to-end anastomosis with interrupted 4–0 PDS sutures (Fig. 1e, patient’s head is left)
Summary
Background Angiomatoid fibrous histiocytoma (AFH) is a soft-tissue tumor that generally affects the extremities of children and young adults, but occasionally occurs at unusual locations such as the trachea [1,2,3]. This case-report demonstrates the challenge in making a correct (histological) diagnosis of endotracheal AFH and presents the first case of successful hybrid bronchoscopic and surgical resection of endotracheal AFH. * Correspondence: w.bouma@umcg.nl 1Department of Cardiothoracic Surgery, University of Groningen, University Medical Center Groningen, Groningen, The Netherlands Full list of author information is available at the end of the article mechanical ventilation she received formoterol and beclomethasone.
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