Abstract
Solitary fibrous tumour (SFT) is a rare oncological entity that most often arises in the pleura. Over the past 10 years, the tumour has been described at numerous extrapleural locations. We present the case of a 42-year-old female Caucasian patient with an extrapleural SFT located at the anterior thoracic wall for 22 years, with atypical histological characteristics and clinical features of malignancy. Management consisted of a wide surgical resection, plastic reconstruction, and postoperative radiotherapy. Although extrapleural SFT usually behaves as a benign soft tissue tumour, it can also present with a more aggressive local behavior, including locoregional recurrence or metastasis. In that case, a multidisciplinary approach is required for accurate diagnosis and proper management.
Highlights
Extrapleural Solitary fibrous tumour (SFT) account for 0.6% of all soft tissue tumours [1]
Extrapleural SFTs account for 0.6% of all soft tissue tumours [1]
SFT is an uncommon neoplasm of mesenchymal origin that was first recognized by Klemperer and Rabin as a distinctive pleural lesion in 1931 [8]
Summary
Malignant extrapleural SFT is an even more rare neoplasm and has been described only in limited series [2, 3] and case reports [4,5,6]. In a large case series of SFTs, Gold et al [1] reported that no difference exists between intrathoracic SFT and extrapleural SFT regarding rates of malignant pathological features but extrapleural SFTs had a significantly higher rate of locoregional recurrence suggesting a more aggressive clinical behavior. In a more recent study of Cranshaw et al [7] 55% of extrapleural SFTs of this series showed malignant features. We hereby present the unusual case of a 42-year-old patient presented with a large, histologically malignant SFT of the anterior thoracic wall
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