Abstract
Hirayama disease is a rare non-progressive spinal muscular atrophy related to flexion movements of the neck. It is considered a benign motor neuron disorder with a stationary stage after a progressive course. We report a case of an 18-years old male with a history of asymmetric weakness and amyotrophy of the distal right upper extremity, suggestive of Hirayama disease. Magnetic resonance imaging (MRI) of the cervical spine was obtained both in flexion and neutral position. MRI showed loss of cervical lordosis with focal areas of lower cervical cord atrophy with increased T2 signal intensity of the spinal cervical cord in a neutral position and anterior displacement of the detached posterior dura from the underlying flexion position.
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