HHE syndrome? What does it mean?s

Abstract

The hemiconvulsion-hemiplegia-epilepsy syndrome (HHE) is a partial epilepsy [1], first described by GASTAUT et al. in 1957 [2]. This syndrome, which has become rare, occurs in children under 4 years of age [1, 2]. Its exact etiopathogenesis remains poorly defined. Therefore, the authors consider that a viral infection can cause vascular disorders which, in turn, lead to ischemic lesions explaining the installation of hemiplegia, convulsive seizures, and cytotoxic edema. Others explain these lesions by the recurrence of convulsive seizures or status epilepticus [3].