Herlyn-Werner-Wunderlich Syndrome: About an Uncommon Case Report

Abstract

Herlyn-Werner-Wunderlich syndrome (HWWS), defined by the triad of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis, is a rare Mullerian duct malformation, usually diagnosed after menarche, when symptoms related to haematocolpos arise. HWW generally occurs at puberty and exhibits variable symptoms including pelvic pain shortly following menarche, dysmenorrhoea, palpable mass due to the associated haematocolpos or haematometra or haemoperitoneum due to retrograde menstruation. Ultrasonography and MRI are extremely useful in the diagnosis and classification of Müllerian duct anomalies. 3D ultrasound is more effective in the diagnosis of uterine malformation. Early detection of this relatively rare syndrome can lead to the provision of immediate treatment to preserve future fertility. We present a rare case report on Herlyn-Werner-Wunderlich syndrome from Morocco.