Abstract
Background: Herlyn-Werner-Wunderlich syndrome (HWWS) is a rare type of female reproduction tract malformation, often accompanied by abnormal development of the ipsilateral urinary system, which shows mostly double uterus and the absence of the kidney on the oblique side. Case Report: An 11-year-old patient presented with lower abdominal distension and pain for 2 days and was suspected of vaginal haematoma. Conclusion: Ipsilateral renal agenesis was confirmed by ultrasound during hospitalization, and the diagnoses of obstructed hemivagina and ipsilateral renal anomaly syndrome were established. The aim of this study was to present the diagnostic and therapeutic approaches in HWWS, and to draw attention to the challenges in its diagnosis, which can coexist with multiple complications.
Highlights
Herlyn-Werner-Wunderlich syndrome (HWWS; known as Oblique vaginal septum syndrome, OVSS) is a kind of asymmetric genitourinary congenital malformations, including didelphys uterus, unilateral blind hemivagina, and ipsilateral renal agenesis, such as absence of one side of the kidney, which is more common in HWWS, heterotopic single kidney malformation, horseshoe kidney, etc. [1] [2]
Ipsilateral renal agenesis was confirmed by ultrasound during hospitalization, and the diagnoses of obstructed hemivagina and ipsilateral renal anomaly syndrome were established
The vagina is formed by the development and connection of the end of the accessory mesonephric duct and the urogenital sinus
Summary
Herlyn-Werner-Wunderlich syndrome (HWWS; known as Oblique vaginal septum syndrome, OVSS) is a kind of asymmetric genitourinary congenital malformations, including didelphys uterus, unilateral blind hemivagina, and ipsilateral renal agenesis, such as absence of one side of the kidney, which is more common in HWWS, heterotopic single kidney malformation, horseshoe kidney, etc. [1] [2]. Herlyn-Werner-Wunderlich syndrome (HWWS; known as Oblique vaginal septum syndrome, OVSS) is a kind of asymmetric genitourinary congenital malformations, including didelphys uterus, unilateral blind hemivagina, and ipsilateral renal agenesis, such as absence of one side of the kidney, which is more common in HWWS, heterotopic single kidney malformation, horseshoe kidney, etc. A case of HWWS patient admitted to the First Affiliated Hospital of Yangtze University, the First People’s Hospital of Jingzhou is reported, combined with literature review, in order to strengthen clinicians’ understanding of this syndrome, improve the diagnosis rate of HWWS, and improve the prognosis of patients. Herlyn-Werner-Wunderlich syndrome (HWWS) is a rare type of female reproduction tract malformation, often accompanied by abnormal development of the ipsilateral urinary system, which shows mostly double uterus and the absence of the kidney on the oblique side.
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