Abstract
Hemophilic pseudo tumors are rare, but well known complication of severe hemophilia, which most frequently develop at the femur, tibia, pelvic bones.
Highlights
Hemophilic pseudo tumors are rare, but well known complication of severe hemophilia, which most frequently develop at the femur, tibia, pelvic bones [1]
A-38-year-old male diagnosed as congenital Hemophilia A since 1985 with history of multiple bleeding episodes and transfusions with factor VIII concentrates presented with complaints of left sided limping and lump sensation over left lumbar area for 10 months, initially of the size of coconut that gradually enlarged to present massive size (Figures 1A and 1B) despite receiving multiple factor VIII concentrates
With a goal to raise factor VIII activity to 80% he was transfused with Factor VIII concentrates and excision of pseudotumor was done without intra/postoperative complications
Summary
Hemophilic pseudo tumors are rare, but well known complication of severe hemophilia, which most frequently develop at the femur, tibia, pelvic bones [1]. A-19-year-old male being symptomatic since the age of 2 years for recurrent episodes of epistaxis and bleeding into major joints predominantly of knee and elbow and being diagnosed as Hemophilia B with history of multiple transfusions of fresh-frozen-plasma and factor IX concentrates in past He came for complaints of gradually increasing distension of right sided abdomen (Figures 2A and 2B). Lab investigations revealed a PTT prolongation of 30 seconds, normal liver and renal function tests His viral markers were negative, factor IX levels less than 1% (severe hemophilia B) with no inhibitor antibodies detected and CECT abdomen (Figures 2A and 2B) showed large hyper dense lesion of approximately 20×20 centimeters occupying the right hypochondriac, paraumblical and lumbar region suggestive of Postoperativeday Factor VIII Factor VIII Factor VIII dosage level level (Trough level) (Peak level). This patient was given factor IX concentrates with similar factor IX levels being maintained thorough out the course of his hospital without intra or post-operative complications
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