Hemiplejía aguda infantil por obstrucción arterial intracraneal múltiple y progresiva

Abstract

The case presented is a clinical and angiographic study of a 5-year-old girl acutely afflicted by right hemiplegia and aphasia. Data from consecutive cerebral angiograms disclosed unequivocally the existence of multiple and progressive arterial occlusions. Similar syndromes have originally been reported by several Japanese authors. The authors found no reported cases of this type in the Spanish literature. This case is especially interesting because it lacks the oriental ancestry which was thought by some authors to be a prerequisite for the disease. The pathogenesis of this syndrome is specifically discussed from the following aspects: the development of an extensive collateral vascular network, the type and location of the arterial obstructions, the course of the disease, and the possible aetiological factors. The possibilities are discussed as to whether the condition is due to a congenital malformation or is acquired or is due to a combination of both factors. The authors feel that before any conclusion can be drawn concerning the aetiology of this rare disease further pathological studies are imperative.