Abstract
Myxomas are low-prevalence heart tumors in the pediatric population. They are located in the left atrium in 75-86% of cases, and 30-50% are accompanied by general symptoms such as fever, weight loss, myalgias, arthralgias and elevated inflammatory markers caused by IL-6 release. They are rapidly growing heart tumors, and their most important complications are valvular and ventricular inflow tract obstruction, which may cause sudden death. Three to ten percent of cases are associated with Carney complex (CNC), type 1, caused by a mutation of the PRKAR1A gene on chromosome 17.
Highlights
Showed a hemoglobin of 7.5 g/dl, normal leukocytes and platelets, and negative inflammatory markers and blood cultures
Myxomas are low-prevalence heart tumors in the pediatric population. They are located in the left atrium in 75-86% of cases, and 30-50% are accompanied by general symptoms such as fever, weight loss, myalgias, arthralgias and elevated inflammatory markers caused by IL-6 release
We present the case of a 10-year-old girl with general symptoms, a murmur, syncope, hemolytic anemia and multiple nevi, in whom a giant obstructive myxoma was found in the left atrium
Summary
Showed a hemoglobin of 7.5 g/dl, normal leukocytes and platelets, and negative inflammatory markers and blood cultures. She underwent surgery with partial resection of the interatrial septum, complete transeptal tumor resection, and interatrial septum reconstruction with an autologous pericardial patch, with no complications. Echocardiographic follow up showed minimal MR and no residual tumor. She was discharged from our center after 21 days, without complications. She is currently in follow up and the family is being studied for CNC, type 1
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