Giant Naevoid Syringocystadenoma Papilliferum

Abstract

Sir, Syringocystadenoma papilliferum (SCAP) is a rare tumour first described in 1893 (1). To date, 400 cases have been reported worldwide. SCAP usually appears at birth or in early childhood, most frequently on the face or scalp. In approximately 25% of cases it is observed on other locations such as the trunk or the extremities. In 40% of cases, SCAP evolves contiguous to a pre-existing naevus sebaceous, but cases without an antecedent naevus sebaceous have also been described (2). In 10% of cases SCAP was associated with naevus sebaceous and a basal cell carcinoma. SCAP typically consists of one papule to several papules in a linear arrangement or alternatively as a solitary plaque. Macroscopically, the mature lesion consists of clusters of generally pinkish brown nodules 2–10 mm in diameter with an occasional central opening. During puberty, SCAP may increase in size and develop a crusted and papillomatous texture (3). Here, we report the case of a giant naevoid SCAP that did not develop malignancy despite a long disease course and an absence of medical treatment.