Abstract

目的:提高巨淋巴结增生症的认识水平.方法:通过2例经手术及病理证实的巨淋巴结增生症的病例分析,结合文献复习,对本病的病因、临床表现、病理、诊断与鉴别诊断、治疗及预后进行讨论.结果:巨淋巴结增生症是一种异源性的罕见的淋巴组织增生性良性疾病.其组织形态上可分为透明血管型和浆细胞型两类,前者常表现为纵隔病变,后者好发于肠系膜和腹膜后淋巴结.结论:该病为少见病,病因尚不明确,患者多无症状,首选治疗为手术切除,预后好.

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