Giant Ameloblastoma of the Mandible: An Exceptional Case Reports in the Early Childhood

Abstract

Ameloblastoma is an odontogenic epithelium tumor very rare in children. It is histologically benign with locally extensive potential justifying the nickname “benign tumor with local malignancy”. The aim of our study was to start from a clinical case data and tried to bring out key elements of a specific therapeutic approach in children. We report the observation of a 5 y old girl, weighing 16 kg with a height of 1.05 m and presenting a voluminous tumor of the left mandible. The history taking noted the up raising marked by a progressive painless increase in size of the mandible without dental malocclusion, five months earlier. In her background check we noticed complete vaccination, heterozygote sickle cell disease at her 59 y old father. The examination found asymmetry of the lower part of the face and a voluminous mass blowing the alveolar rampart of the left mandible. The medical imaging evoked the diagnosis and histology after excision confirmed ameloblastoma. Then, reconstruction of the loss of bone by an inferior pedicled Facial Artery Muscular Mucosal (FAMM) flap was performed in the 24th postoperative day. There wasn’t distant recurrence of the tumor after 4 y follow up. The clinical feature is the age of our patient, the giant aspect of the tumor at the diagnosis time and the recourse to the FAMM flap for filling bone loss.