Frontonasal dysplasia and its orodental aspects

Abstract

The case is reported of a 4 1/2-year-old black female with macrocephaly and frontonasal dysplasia, characterized by ocular hypertelorism, a broad nasal bridge, a partially bifid nose, and some asymmetry of the facial bones. Orally, she showed a definite tendency toward mandibular retrognathism with a developing malocclusion. Although only 4 1/2 years old she had an advanced dental age of at least 6 years with the early eruption of the left maxillary incisor and two lower permanent incisors. Her early dental development was symmetrical and evident in all four quadrants.