Fibrous dysplasia of temporal bone.

Abstract

WE ARE PRESENTING a rare instance of monostotic fibrous dysplasia primarily involving the temporal bone which by subsequent enlargement caused displacement of the mandible. Review of the literature reveals only three reported cases of monostotic fibrous dysplasia with primary temporal bone involvement. Review of Fibrous Dysplasia The term fibrous dysplasia is a general term indicating a tumor-like lesion or hamartoma replacing one or more bones with fibrous tissue. Fibrous dysplasia is generally distinguished in two clinical varieties: the polyostotic or generalized form in which several bones are affected and the monostotic form where only one bone or restricted bone area is involved. The first reports of this condition were by Albright et al1who described patients with multiple bone lesions of the osteitis fibrosa type, pigmentation of skin, and endocrine disorders, and subsequently this disorder was called Albright's disease. Lichtenstein2later termed this disorder polyostotic fibrous dysplasia. Present