Abstract
Fibromuscular dysplasia is a nonatherosclerotic and non-inflammatory vascular disease with primary lesion of renal and internal carotid arteries. We present a neonatal case of fibromuscular dysplasia who died on the second day of life. The newborn suffered from fibromuscular dysplasia of the coronary arteries and a congenital heart defect. The interesting feature of this case was the formation of aneurysms of the coronary arteries with pulmonary atresia. This case demonstrates a casuistically rare form of association between fibromuscular dysplasia of the coronary arteries and pulmonary artery atresia.
Highlights
Fibromuscular dysplasia (FMD) is a nonatherosclerotic and non-inflammatory vascular disease with primary lesion of renal and internal carotid arteries
The described case shows the unique data about FMD
FMD involving the coronary arteries has been verified in separate cases
Summary
Fibromuscular dysplasia (FMD) is a nonatherosclerotic and non-inflammatory vascular disease with primary lesion of renal and internal carotid arteries. FMD was first described by Leadbetter and Burkland in 1938. They observed a 5-year old boy with hypertension and atrophy of the right kidney. The term “fibromuscular hyperplasia” was introduced in 1958 by McCormack et al The authors collected four cases of “fibromuscular hyperplasia” over 20 years and first described in detail the essence of the pathological changes [2]. FMD is a rare disease with a variety of pathological changes in the affected arteries and all cases require detailed investigation. The aim of our researсh was to analyze a rare case of fibromuscular dysplasia of the coronary arteries and compare it with the literature
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