Fibrocystic disease of the pancreas: roentgen manifestations.

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Fibrocystic disease of the pancreas is a hereditary, generalized, glandular disease of children manifested by pancreatic deficiency, chronic pulmonary lesions, disturbances of the sweat and salivary excretion, and cirrhosis of the liver. Involvement may be multiple or single. The condition is limited almost entirely to the Caucasian race; it is rarely found in Negroes and never in Mongolians. Though the name suggests a primary disease of the pancreas, this is misleading, since almost all of the exocrine glands are involved. Common usage, however, precludes any change in nomenclature at this time. Fibrosis of the pancreas is, in any event, an outstanding pathologic finding. Fibrocystic disease of the pancreas occurs about once in 600 live births (1), which means that, out of a total of approximately 4,200,000 live births in the United States in a year, there are 7,000 cases. The Babies Hospital in New York sees about 27 new cases a year and at the Children's Memorial Hospital in Chicago we had 30 cases in ...