Abstract
Purpose: To report a case of familial exudative vitreoretinopathy (FEVR) and discuss the clinical manifestation, angiographic features and treatment of this disease. Method: Interventional case report Result: A healthy 9-year-old boy complained of progressive blurred vision in both eyes for 6 months. The presenting best-corrected visual acuity (BCVA) was 6/10 in the right eye and 6/20 in the left eye. Fundoscopy disclosed bilateral non-rhegmatogenous retinal detachment and subretinal fibrosis. Fluorescein angiography revealed avascular area with neovascularization at temporal periphery in both eyes. The temporal retinal vasculature terminated abruptly with scalloped borders adjacent to the avascular zone. He was born in full term without previous exposure to oxygen therapy. After surgical intervention, retina was attached in both eyes. Final BCVA was 6/60 in the right eye and 6/10 in the left eye. Conclusion: Subretinal fibrosis is an unusual feature in FEVR. Early surgical intervention is beneficial to this disease.
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