Abstract
Bilateral striopallidodentate calcinosis, commonly known as Fahr's disease, is a rare syndrome characterised by symmetrical calcification over the basal ganglion and dentate nucleus. No case of Fahr's disease with associated manic symptoms has been described in the literature to date. We report an unusual case of Fahr's Disease in a 18 year old unmarried male who presented to the emergency department of Universal College of Medical Sciences - Teaching Hospital, Nepal with symptoms of mania. Computed tomographic scan of the patient demonstrated extensive symmetrical calcification over the basal ganglia and dentate nuclei. No underlying cause for the bilateral calcification was found. This rare case of Fahr's disease, which has never been reported in Indian literature has been reported to highlight this unusual condition and its differentiation from the commoner Fahr's syndrome.
Highlights
Fahr’s disease, is a rare neurologic disorder of unknown etiology characterized by neuropsychiatric abnormalities, parkinsonian or choreoathetotic type movement disturbances and extensive symmetrical calcification of the basal ganglia and dentate nuclei in the cerebellum.[1]
We report a case of Fahr’s disease in a 18 year male who presented with symptoms of mania
CT scan is considered to be the best modality of investigation in the diagnosis of Fahr’s disease where unenhanced CT reveals dense calcifications within the basal ganglia, subcortical white matter of the posterior parietal lobes and the dentate nuclei of the cerebellum
Summary
Fahr’s disease, is a rare neurologic disorder of unknown etiology characterized by neuropsychiatric abnormalities, parkinsonian or choreoathetotic type movement disturbances and extensive symmetrical calcification of the basal ganglia and dentate nuclei in the cerebellum.[1]. Fahr’s disease, is a rare neurologic disorder of unknown etiology characterized by neuropsychiatric abnormalities, parkinsonian or choreoathetotic type movement disturbances and extensive symmetrical calcification of the basal ganglia and dentate nuclei in the cerebellum.[1] No case of Fahr's disease with associated manic symptoms has been described in the literature to date. We report a case of Fahr’s disease in a 18 year male who presented with symptoms of mania.
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