Fahr Syndrome: A Rare Case Report

Abstract

Introduction: Fahr syndrome, also known as idiopathic basal ganglia calcification, is a rare neurologic disorder of unknown etiology that presents with various general and oral findings. The purpose of this case report is to discuss the oral and general findings associated with Fahr syndrome.Case Presentation: A 33‐year‐old female patient reported to the Department of Periodontics, Oxford Dental College, Bangalore, India, with a complaint of loose teeth for the prior 6 months. Additional investigation showed a wide array of findings, including stunted growth, altered gait, osteoporosis, and increased thyroxine and thyroid stimulating hormone. Intraoral findings revealed oligodontia and severe chronic generalized periodontitis of the remaining teeth. Complete extraction followed by full‐mouth rehabilitation was planned.Conclusion: This case report highlights the need for a dentist to be well informed about the signs and symptoms of Fahr syndrome to aid in the right diagnosis and treatment plan.