Extreme penoscrotal transposition

Abstract

enoscrotal transposition (PST) is an extremely rare congenital malformation, usually associated with a wide variety of other anomalies. We describe an exceptional case of a newborn with extreme PST and severe hypospadias but normal upper urinary tract and no other associated malformations.A newborn male delivered at term with no reported antenatal complications. Three routine obstetrical sono-graphy showed normal fetal development. There was no evidence of mother being exposed to teratogens during pregnancy. On physical examination, an abnormal appearance of the external genitalia could be seen. There was a complete rotation of the external genitalia with a normal scrotum and testis but a rudimentary penis with a severe proximal hypospadias and chordee just attached anterior to the anal margin. Urinalysis, renal and vesical sonography and voiding cystourethrography showed no other urological abnormalities. There were no associated cardiological or gastrointestinal anomalies.Complete PST is a very uncommon heterogeneous condition in which the scrotum is positioned superior and anterior to the penis. It was fi rst recognized in 1923 by Appleby in an adult patient.