Extragnathic psammous desmo-osteoblastoma of maxilla - A unique entity

Abstract

Juvenile psammomatoid ossifying fibroma (JPOF) is a rare fibro-osseous neoplasm in young children which is locally aggressive, spreads quickly and has a very high recurrence rate. Early detection and complete excision are essential. It generally occurs in extragnathic craniofacial bones such as periorbital, frontal, and ethmoid bones. Jaw bones are rarely involved. Here, we report a case of JPOF of the maxilla in a 16-year-old female patient. Complete surgical excision along with removal of the first premolar was done. It was initially thought to be Fibro-osseous lesions which were provisionally diagnosed as juvenile ossifying fibroma clinically and radiographically but confirmed histopathologically as JPOF. Definitive diagnosis and treatment of such lesions depend on the collective correlation of clinical, radiographic, and histopathological features.