Extradural Low-grade Fibromyxoid Sarcoma With Sacral Body Destruction Causing Cauda Equina Syndrome

Abstract

Low-grade fibromyxoid sarcoma is a rare tumor that most commonly arises from the deep soft tissues of the upper or lower extremities in young men. In this report, we describe a rare case of a low-grade fibromyxoid sarcoma that appeared to develop as a primary malignancy in the extradural area, with sacral body destruction and extension to the paravertebral muscles causing cauda equina syndrome. The patient underwent marginal resection for 2 paravertebral masses and intralesional resection for extradural and bone destructive masses. The diagnosis was made according to the strikingly characteristic microscopic appearance of bland spindle cell sarcoma containing numerous giant collagen rosettes and was further supported by immunohistologic findings.