Abstract
The presentation of extra hepatic biliary-atresia (EHBA) as well as choledochal cyst (CDC) in the neonate may be similar. Since the surgical management and prognosis are entirely different, it is important to differentiate between the two entities. We present a case with co-existing EHBA and CDC which led to a diagnostic dilemma.
Highlights
Surgical causes of neonatal obstructive jaundice include extra hepatic biliary atresia (EHBA) and rarely infantile form of choledochal cyst (CDC) [1]
We present a case of type 3 EHBA (The Japanese Association of Pediatric Surgeons classification) with co-existing Type I CDC (Todani) which led to a diagnostic dilemma
A thorough literature search revealed less than 100 cases of EHBA associated with CDC reported till date [2,3,4,5,6,7,8] of which majority were Type 1-EHBA (76%) and only 21% were Type 3EHBA [2]
Summary
Surgical causes of neonatal obstructive jaundice include extra hepatic biliary atresia (EHBA) and rarely infantile form of choledochal cyst (CDC) [1]. The fasting ultrasonography revealed an enlarged liver with a normal gall bladder (GB) and common bile duct (CBD). CDC associated with Type 1-EHBA has been described only in neonates who are found to have distal atresia of the CBD during intra-operative cholangiogram [3].
Sign-in/Register to view highlights & summary Sign-in/Register to access full text options 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
