Abstract
Extracardiac fetal rhabdomyoma is a rare tumor occurs almost exclusively in children under the age of 10 years with a predilection for the head and neck region and chest wall. It can occur in other sites also. However it is very rare in dorsum of foot. Rhabdomyoma accounts for less than 2% of all striated muscle tumors. Differentiation from Embryonal Rhabdomyosarcoma(ERMS) is very important to avoid aggressive treatment and its consequences. We have reported this case of extracardiac fetal rhabdomyoma of dorsum of foot in an eleven month old male child because of rarity of location which was surgically resected. Histopathology and immunohistochemistry confirmed the diagnosis of extra cardiac fetal rhabdomyoma. DOI: 10.21276/APALM.2017.1045
Highlights
Extracardiac fetal rhabdomyoma are extremely rare benign tumor of striated muscle comprising of less than 2% of all striated muscle tumors.[1]It affects both children and adult that are composed of immature striated muscle at the 6th to 10th week stage of development.[2]
Extracardiac fetal rhabdomyoma of dorsum of foot is very rare. We report this case of fetal rhabdomyoma arising in the dorsum of foot with complete resection in a 11 month old boy which was clinically and radiologically suspected as rhabdomyosarcoma
An eleven month old boy was referred to the department of Paediatric surgery at Gauhati Medical College and Hospital (GMCH) for a small subcutaneous mass at the dorsum of right foot which was initially noticed by the mother and later on she informed paediatrician during child’s regular checkup
Summary
Extracardiac fetal rhabdomyoma are extremely rare benign tumor of striated muscle comprising of less than 2% of all striated muscle tumors.[1]It affects both children and adult that are composed of immature striated muscle at the 6th to 10th week stage of development.[2]. Some fetal rhabdomyoma may reccur as rhabdomyosarcoma.[1] Extracardiac fetal rhabdomyoma of dorsum of foot is very rare. An eleven month old boy was referred to the department of Paediatric surgery at Gauhati Medical College and Hospital (GMCH) for a small subcutaneous mass at the dorsum of right foot which was initially noticed by the mother and later on she informed paediatrician during child’s regular checkup. The child underwent complete local excision of the mass and it was sent to the pathology department GMCH for histopathological examination.Grossly it was well circumscribed (4.0X3.5cm) (Fig.1) whitish mass with myxoid cut surfaces. Histopathological findings were of a well circumscribed cellular lesion composed of oval to spindle shaped cells with moderate amount of cytoplasm and bland nuclei in a variable fibromyxoid stroma (Fig.2a,b,c). Till date patient is doing well without any evidence recurrence
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