Exercise and Habitual Physical Activity for People With Cystic Fibrosis

Abstract

Exercise and physical activity have been recommended since the 1970s as important aspects of care for people with cystic fibrosis (CF). Benefits of an active lifestyle for these patients include improved pulmonary function, functional capacity, and quality of life and also decreased mortality. However, there are not currently any guidelines available to CF care centers regarding the type, amount or frequency of exercise, or habitual physical activity that should be performed to achieve these benefits. In addition, there is no guidance available about adapting physical activity and exercise for different ages or comorbidities common to CF. This document presents evidence-based recommendations from an international group of experts in the area of exercise for CF to guide practitioners toward the goal of regular, appropriate habitual physical activity, exercise and sports for all patients with CF. As lifespan for people with CF increases, it is important that regular physical activity is incorporated as part of daily care for a lifetime.