Evaluation of Residual Functional Lung Volume on Tc-99m DTPA Aerosol Ventilation and Tc-99m MAA Perfusion Scintigraphy in Primary Ciliary Dyskinesia (Kartagener Syndrome)

Abstract

Kartagener syndrome is diagnosed as sinusitis, bronchitis (bronchiectasis), and situs inversus by the clinical features. It is a subclass of primary ciliary dyskinesia (PCD) disease. A 12-year-old girl who had frequent upper and lower airway infections since birth, which was confirmed as Kartagener syndrome by HRCT imaging. We present the residual functional lung volume and mucociliary clearance findings seen on Tc-99m DTPA aerosol ventilation and Tc-99m MAA perfusion scintigraphy.