Erythema Elevatum Diutinum: A Rare Dermatosis with an atypical Presentation

Abstract

EED is a form of chronic cutaneous vasculitis of unknown underlying etiology [1]. EED was named by Henry RadcliffCrocker and Williams in 1894 but discovered earlier in 1878 by Hutchinson. It presents clinically as asymptomatic, firm, erythematous to yellowish papules, nodules, or plaques involving the extensor surface of extremities often over joints [1]. Antigeninduced small vessel vasculitis is believed to be the cause. Various infections and systemic disorders like streptococcal throat infection, tuberculosis, HIV 1, HIV 2, Hepatitis B, Rheumatoid arthritis, ankylosing spondylitis, Sarcoidosis, Crohn’s disease, Ulcerative colitis, Pyoderma gangrenosum, Paraproteinemia, Myelodysplasia, Kaposi’s sarcoma have been reported to be associated [1]. The clinical presentation of EED varies as the lesions progress leading to diagnostic difficulties [1].