Abstract
Erdheim-Chester disease is an unusual syndrome characterized by non-Langerhans cell histiocytosis which can mimic rheumatologic diseases. We report a case of Erdheim-Chester masquerading as giant cell arteritis, which was success-fully managed with anakinra as anti IL-1 therapy.
Highlights
Erdheim-Chester disease is an unusual syndrome characterized by non-Langerhans cell histiocytosis which can mimic rheumatologic diseases
We report a case of Erdheim-Chester masquerading as giant cell arteritis, which was successfully managed with anakinra as anti IL-1 therapy
We report for the first time a case of Erdheim-Chester disease with histologic evidence of temporal artery inflammation in a patient who had symptoms of giant cell arteritis
Summary
Erdheim-Chester disease is an unusual syndrome characterized by non-Langerhans cell histiocytosis. It is a systemic disorder with a plethora of symptoms and signs. We report for the first time a case of Erdheim-Chester disease with histologic evidence of temporal artery inflammation in a patient who had symptoms of giant cell arteritis
Sign-in/Register to view highlights & summary Sign-in/Register to access full text options 
Free) 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a call
