Epsilon-aminocaproic acid in the reversal of consumptive coagulopathy with platelet sequestration in a vascular malformation of klippel-trenaunay syndrome

Abstract

We herein report the successful use of epsilon-aminocaproic acid to reverse the thrombocytopenia and coagulopathy in a girl with the Klippel-Trenaunay syndrome. The efficacy of the treatment was associated with thrombosis and obliteration of the abnormal vascular channels