Abstract
Epithelioid sarcoma is a rare malignant soft tissue neoplasm commonly involving extremities of young adults and rarely occurring in the trunk area. It re-sembles a chronic inflammatory process and mimics benign reactive granuloma or other benign diseases. Despite its indolence and slow growth, the prognosis is poor with high recurrence and early lymph node spreading and hematogeneous distant metastasis. Involvement of the spine is extremely rare and diffi-cult to diagnose correctly in clinical presentation and pathology. We describe our experience a case of epi-thelioid sarcoma involving lumbar spine. A pre-ope- rative spine MRI showed a large solid and necrotic paraspinal mass which extended into the spinal canal with cord compression, and bone destruction. Final correct diagnosis was confirmed by immunohisto-chemical studies. When young adults present with a spinal lesion that has unusual large necrotic soft tissue mass, immunohistochemical studies are recommended for promptly determining the possibility of spinal epithelioid sarcoma.
Highlights
Epithelioid sarcoma is a rare malignant soft tissue neoplasm which occurs most commonly in the extremities in young adults [1,2,3,4,5]
We describe our experience a case of epithelioid sarcoma involving lumbar spine
The prognosis of epithelioid sarcoma is poor because it has extreme aggressiveness and has a high tendency for local recurrence and lymphatic or hematogeneous metastasis [1,2,3,5,6,7,8]
Summary
Epithelioid sarcoma is a rare malignant soft tissue neoplasm which occurs most commonly in the extremities in young adults [1,2,3,4,5]. The diagnosis of epithelioid sarcoma has been considered difficult both for clinicians and pathologists because of its relative indolence and slow growth, as well as resemblance to other benign tumors [2,3,4]. The prognosis of epithelioid sarcoma is poor because it has extreme aggressiveness and has a high tendency for local recurrence and lymphatic or hematogeneous metastasis [1,2,3,5,6,7,8]. Spinal epithelioid sarcoma is extremely rare [9,10] and is very difficult to diagnose correctly [2,3,4,8,9,10]. We report a case of epithelioid sarcoma of the lumbar spine with review of literature
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