Epithelioid Hemangioendothelioma of the Pisiform

Abstract

The term epithelioid hemangioendothelioma (EH) was first identified and described in 1982 by Weiss and Enzinger [15] for a rare endothelial vascular neoplasm in soft tissues with a histologic appearance and clinical course between hemangioma and angiosarcoma. EH of the bone is extremely rare, with a 1 % incidence among all vascular bone tumors, and usually involves the skull, spine, femur, tibia, and feet of adults [1, 5, 8]. EH involving bones of the hand is exceptional, with only four cases previously reported [10, 14]. We report a case of HE involving the pisiform bone. To our knowledge, this is the first case that has been reported.