Epithelioid Hemangioendothelioma arising from nasal cavity: A Rare Case

Abstract

Introduction: Epithelial Hemangioendothelioma is an uncommon malignancy of soft tissues, mostly occur in females in their 4th and 5th decades of life. It is very rare to occur in nasal cavity and prone to have local recurrences and distant metastasis. Here we present a 37 year old male patient with epithelioid hemangioendothelioma in nasal cavity with extension to the surrounding structures. Case report: Patient presented to University Hospital - Kotelawala Defense University with a history of right side nasal obstruction, facial pain and headache. Imaging studies showed large focal lesion with extension to the surrounding structures and impending intracranial extension. Endoscopy and neuronavigator guided tumor excision done and histopathology report came as epithelioid hemangioendothelioma. Conclusion: Radical local excision is the key important step in the management of Epithelioid hemangioendothelioma.