Abstract
Infantile Hemangioendothelioma of the liver is an uncommon tumor. Two subtypes have been described. Type1 has recognizable but irregularly dilated vascular spaces in a fibromyxomatous stroma. Type 2 is described as having a more aggressive histology. It is marked by poorly formed and anatomising channels with papillae lined by atypical endothelial cells and is potentially malignant. Clinical presentation is variable, hepatomegaly or abdominal mass, some hematological abnormalities may be seen. In laboratory investigation, or lesion may be asymptomatic and discovered incidentally. We report a case of 45 day old female child who presented with abdominal distension. CT abdomen showed hypoattenuating mass in the left lobe of the liver along with specks of calcification.. The mass was excised and had large areas of gritty calcification simulating a teratoma. however histopathological diagnosis of infantile hemangioendothelioma type I of liver was made. Hemangioendothelioma of the liver has been reported as most common benign symptomatic vascular tumor of the liver in infancy.
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