English

Abstract

Mal de Meleda is a rare autosomal recessive palmoplantar keratoderma characterized by transgradient keratoderma with associated scleroatrophy, knee changes and onychogryphosis. This case of a 20 year old girl born of second degree consanguineous marriage is reported for its uniqueness in conformity with criteria enunciated by Stulli associated with hyperkeratotic warty papules clinically fitting into Darier's disease with lip involvement. Another interesting feature being black pigmentation of fingers and nails which was due to cashew nut shell paste application mistaken for dry gangrene.