English

Abstract

We report successful anaesthetic management of a patient with hereditary spherocytosis who underwent laproscopic splenectomy, cholecystectomy and appendioectomy. Hereditary spherocytosis is a familial hemolytic disorder with marked heterogeneity of clinical features, ranging from asymptomatic condition to a fulminant hemolytic anaemia. Commonly recommended perioperative management in these patients includes preemptive erythrocyte transfusion, aggressive hydration and avoidance of hypoxia, aplastic crisis, hypothermia and acidosis. The management of such a case is challenging from anaesthetic point of view because