Ebstein's Malformation of the Tricuspid Valve Associated with Valvular Stenosis and Cor Triatriatum

Abstract

Ebstein's malformation of the tricuspid valve tends to occur as an isolated condition except for the common association of a patent foramen ovale. Nevertheless, several other conditions may be associated with Ebstein's anomaly. These include ventricular septal defect, 1 Vacca JB Bussmann DW Mudd VG Ebstein's anomaly: Complete review of 108 cases.. Am J Cardiol. 1958; 2: 210-226 Abstract Full Text PDF PubMed Scopus (28) Google Scholar pulmonary stenosis with or without a ventricular septal defect, 2 Schiebler GL Adams P Jr Anderson RC Clinical study of 23 cases of Ebstein's anomaly of the tricuspid valve.. Circulation. 1959; 19: 165-187 Crossref PubMed Scopus (50) Google Scholar pulmonary atresia with intact ventricular septum, 3 Caddell JL Browne MJ Right ventricular hypertension and pulmonary stenosis in Ebstein's anomaly of the heart.. Am J Cardiol. 1963; 11: 100-106 Abstract Full Text PDF PubMed Scopus (4) Google Scholar and several transposition syndromes. 4 Becu LM Swan HJC DuShane JW Cardiac clinics. CXLIV. Ebstein malformation of the left atrioventricular valve in corrected transposition of the great vessels with ventricular septal defect.. Proc Staff Meet Mayo Clin. 1955; 30: 483-490 PubMed Google Scholar Most of these anomalies are not commonly associated with Ebstein's malformation, and pulmonary valvular stenosis is rare in the absence of ventricular septal defect. 5 De Leon AC Jr Perloff JK Blanco P. Congenital pulmonic stenosis complicating Ebstein's anomaly of the tricuspid valve.. Am J Cardiol. 1964; 14: 695-701 Abstract Full Text PDF PubMed Scopus (9) Google Scholar The purpose of this report is to describe the clinical and pathologic features of a case of Ebstein's malformation associated with a rare combination of anomalies, namely, valvular pulmonic stenosis and cor triatriatum.