Dystrophic Scoliosis in Neurofibromatosis and Rib-head Resection: A Case Report.

Chong Kl,Zuki Z,Lam Ks

doi:10.5704/moj.1711.007

Chong Kl, Zuki Z + Show 1 more

Open Access

https://doi.org/10.5704/moj.1711.007

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Abstract

Surgical management of scoliosis in Neurofibromatosis type I may be challenging at times especially when dealing with dystrophic curves. We highlight the importance of meticulous study of the radiological imaging and careful pre-operative planning in a patient with dystrophic scoliosis.

Highlights

Scoliosis in neurofibromatosis (NF) can present as a simple straight forward scoliosis or complicated dystrophic scoliosis[1]
Dystrophic scoliosis requires detailed study of the radiological images to identify the presence of dystrophic features because severe dystrophic changes are associated with faster deterioration of the curve progression and to prevent neurological complications peri-operatively[2,3]
Neurofibromatosis is an autosomal dominant chromosomal disorder characterized by scoliosis, café-au-lait spots, pseudarthrosis of long bones and limb overgrowth

Summary

Introduction

Scoliosis in neurofibromatosis (NF) can present as a simple straight forward scoliosis or complicated dystrophic scoliosis[1]. Dystrophic scoliosis requires detailed study of the radiological images to identify the presence of dystrophic features because severe dystrophic changes are associated with faster deterioration of the curve progression and to prevent neurological complications peri-operatively[2,3].

Results

Conclusion