Dyschromatosis Universalis Hereditaria: A Rare Case Report in Southern India

Abstract

Dyschromatosis Universalis Hereditaria (DUH) is a rare genodermatosis characterised by hyper and hypo pigmented macules in reticulate pattern. The clinical manifestations includes occurrence of lesions at the trunk and extremities as the dominants sites. The lesions may spread to the face, hands and feet. Hair, teeth, nails, palms and soles may also be involved. Here, we present a case of 7 year old male patient with DUH with the involvement of whole body surface. The treatment pattern in this case includes cortisol hormone replacement therapy with the use of hydrocortisone tablets for a long period of time.