Dynamic monitoring of a patient with idiopathic pulmonary haemosiderosis

Abstract

Idiopathic pulmonary haemosiderosis (IPH) is one of the causes of alveolar hemorrhagic syndrome in adults; it is extremely rare. The results of clinical observation of a 42-year-old IPH patient with recurrent pulmonary hemorrhage in dynamics (within six months) are presented. The examination revealed anemia, bilateral infiltration process in the lungs, respiratory failure (SpO 2 – 82% in the air). Differential diagnosis was made with autoimmune and non-immune causes of alveolar hemorrhagic syndrome. IPH confirmed by a percutaneous lung parenchyma biopsy. The patient has been successfully treated with systemic glucocorticosteroids in high doses.